Immunoglobulin deficiencies: the B-lymphocyte side of DiGeorge Syndrome.
نویسندگان
چکیده
DiGeorge syndrome is associated with a T-lymphocyte immunodeficiency. The prevalence of hypogammaglobulinemia has not been reported. We found that 3% of patients with DiGeorge syndrome were receiving immunoglobulin replacement therapy and 6% of patients over the age of 3 years had hypogammaglobulinemia. We conclude that DiGeorge syndrome is associated with significant humoral immune deficiency.
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عنوان ژورنال:
- The Journal of pediatrics
دوره 161 5 شماره
صفحات -
تاریخ انتشار 2012